Current position in this corpus

Long-read WGS adds the most diagnostic value in rare disease when the likely mechanism involves structural complexity, dead zones, phasing problems, methylation, or hard-to-map medically relevant genes.

Strong supporting sources

Working synthesis

  • Targeted use is strongly supported for immunodeficiency-like dead-zone cases, structurally complex CNV cases, and unresolved rare disease cases after negative short-read testing.
  • A broader unified-platform argument is also supported, especially when long-read WGS can replace multiple follow-up assays by combining small variants, SVs, phasing, and methylation.
  • Population SV resources appear increasingly useful as filtering aids in rare disease interpretation.

Main tension

Open questions

  • Which phenotype classes should be first-line candidates for long-read WGS?
  • How much additional yield comes from methylation, phasing, and SV detection separately?